Over-the-Counter Antioxidant Improves Symptoms
in Model of ALS
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WESTPORT, Sep 12 (Reuters Health) - N-acetyl-L-cysteine
(NAC), an agent that increases levels of
the antioxidant glutathione, improves survival
and delays onset of motor impairment in a
mouse model of familial amyotrophic lateral
sclerosis (ALS), according to US-based researchers.
Dr. Ashley I. Bush from Harvard Medical School
in Boston and colleagues there and elsewhere
explain that previous studies have shown
that a mutation in copper/zinc superoxide
dismutase (SOD1), which leads to increased
levels of oxidative damage, has been implicated
in the pathogenesis of ALS.
In the present study, the authors investigated
the effects of NAC in transgenic mice with
a mutation in SOD1. Treatment with 1% NAC
in drinking water significantly improved
"both rotorod performance and survival,"
according to the paper published in the August
3rd issue of NeuroReport.
The study team points out that previous research
has shown that 50 mg/kg/day NAC has beneficial
effects in patients with limb-onset sporadic
ALS.
In light of these results and their own findings
Dr. Bush's team suggests that "further
trials of oral NAC supplementation may be
worth considering at higher doses, and possibly
combining it with other safe over-the-counter
supplements that specifically enhance the
activity of the glutathione system."
NeuroReport 2000;11:2491-2493.